Título

Feeder vessel ligature as a surgical treatment for retinal capillary hemangioblastoma in patients with von Hippel-Lindau disease: Case Series.

Introdução

To describe cases of Von Hippel Lindau patients with retinal capillary hemangiomas surgically treated with posterior pars plana vitrectomy and feeder vessel ligature, at the Oncology Ocular Clinic of the Department of Ophthalmology and Visual Sciences of UNIFESP/EPM from March 2017 to March 2018 in association with Retina Clinic, São Paulo.

Método

Retrospective review of medical records from the Ocular Oncology service at the Department of Ophthalmology and Visual Sciences, Federal University of São Paulo from March 2017 to March 2018.

Resultados

The surgery was performed in four eyes of three patients with retinal capillary hemangiomas. The patients were two women and one man aged 14-23 that had not undergone any previous treatment, and that had severe retinal complications due to the capillary hemangiomas, such as Serous Retinal Detachment (75%), Macular Exudation (50%) and Retinal Fibrosis (50%). Before the silicon oil removal it was observed an improvement in the BCVA in 75% of the patients, but this result did not remain stable after the removal of the silicon oil, when 100% of the eyes suffered new Retinal Detachments.

Conclusões

Patients with Von Hippel Lindau have a high risk of visual loss due to capillary hemangioblastomas and its complications. The groups with advanced retinal disease, can be treated with posterior pars plana vitrectomy and feeder vessel ligature, as an attempt to control the disease and maintain some visual acuity. This case series demonstrated the challenges of this surgical technique in treating these patients, and that this technique needs further studies and improvement to be chosen as a safe procedure.