Título / Title

IRVAN SYNDROME: CASE REPORT

Introdução / Purpose

Clinical discussion on Irvan syndrome, a rare entity with a diagnosis based on several clinical findings.

Material e Método / Methods

We report a case of low unilateral major visual acuity secondary to massive macular exudation and telangiectasias in a young adult male patient

Resultados / Results

We demonstrated the diagnostic criteria for this syndrome, treatment and evolution.

Discussão e Conclusões / Conclusion

The diagnosis of the syndrome characterized by idiopathic retinal vasculitis, aneurysms and neuroretinitis (IRVAN) is based on the presence of several clinical findings. Three major criteria (retinal vasculitis, aneurysmal dilatations in arterial bifurcations and neuroretinitis), and 3 minor criteria (non-peripheral capillary perfusion, retinal neovascularization and macular exudation) have already been well defined and are used to aid in the diagnosis of NARF. This is a rare clinical entity whose typical alterations have already been well characterized and its clinical staging already proposed previously .
Initially, it was believed to be a benign, self-limiting condition; however, it is now known that this condition can lead to severe visual loss when not properly diagnosed and treated .The patient described in this case was treated with panphotocoagulation and although he had control of the disease with telangiectasis regression, there was no improvement in visual acuity due to photoreceptor damage due to chronic exudation.

Palavras Chave

Uveitis; Retinitis/diagnosis; Aneurysm/diagnosis; Retinal vasculitis/diagnosis; Fluorescein angiography; Syndrome; Humans; Male; t; Case reports